Q89.81: Kabuki syndrome
Q89.81 is the billable ICD-10-CM diagnosis code for Kabuki syndrome. It is a fully specified code, so it can be reported on a claim (subject to clinical documentation and your payer's rules).
Frequently asked questions
What is ICD-10-CM code Q89.81?
Q89.81 is the ICD-10-CM diagnosis code for Kabuki syndrome. It belongs to category Q89 (Other congenital malformations, not elsewhere classified).
Is Q89.81 a billable code?
Yes. Q89.81 is a billable, fully specified ICD-10-CM code, so it can be used on a claim (subject to documentation and payer rules).
What category does Q89.81 belong to?
Q89.81 is part of ICD-10-CM category Q89 — Other congenital malformations, not elsewhere classified, which has 20 billable codes.
More free billing tools: all ICD-10 categories · ICD-10 search · denial codes · Medicare fees
Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
Code the diagnosis right
Join providers across the country delivering modern virtual care with CareNiva. Free to start, ready in minutes.
100% Satisfaction Guaranteed — try it risk-free