Q89: Other congenital malformations, not elsewhere classified
Codes under Q89 (Other congenital malformations, not elsewhere classified). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| Q89.0 | Congenital absence and malformations of spleen | — |
| Q89.0 | Congenital absence and malformations of spleen | — |
| Q89.01 | Asplenia (congenital) | ✓ |
| Q89.01 | Asplenia (congenital) | ✓ |
| Q89.1 | Congenital malformations of adrenal gland | ✓ |
| Q89.1 | Congenital malformations of adrenal gland | ✓ |
| Q89.2 | Congenital malformations of other endocrine glands | ✓ |
| Q89.2 | Congenital malformations of other endocrine glands | ✓ |
| Q89.3 | Situs inversus | ✓ |
| Q89.3 | Situs inversus | ✓ |
| Q89.4 | Conjoined twins | ✓ |
| Q89.4 | Conjoined twins | ✓ |
| Q89.7 | Multiple congenital malformations, not elsewhere classified | ✓ |
| Q89.7 | Multiple congenital malformations, not elsewhere classified | ✓ |
| Q89.8 | Other specified congenital malformations | — |
| Q89.8 | Other specified congenital malformations | — |
| Q89.09 | Congenital malformations of spleen | ✓ |
| Q89.09 | Congenital malformations of spleen | ✓ |
| Q89.9 | Congenital malformation, unspecified | ✓ |
| Q89.9 | Congenital malformation, unspecified | ✓ |
| Q89.81 | Kabuki syndrome | ✓ |
| Q89.81 | Kabuki syndrome | ✓ |
| Q89.89 | Other specified congenital malformations | ✓ |
| Q89.89 | Other specified congenital malformations | ✓ |
Frequently asked questions
What is ICD-10-CM code Q89?
Q89 is an ICD-10-CM category covering Other congenital malformations, not elsewhere classified. It contains 24 more specific diagnosis codes, 20 of which are billable.
Is Q89 a billable code?
No — Q89 is a category header and isn't billable on its own. Code to the highest level of specificity using one of its subcodes (for example Q89.0 — Congenital absence and malformations of spleen). 20 of the 24 codes under Q89 are billable.
What codes fall under Q89?
Q89 includes Q89.0, Q89.0, Q89.01, Q89.01, Q89.1, plus 19 more. See the full list with descriptions and billable status above.
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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