Q87: Other specified congenital malformation syndromes affecting multiple systems

Codes under Q87 (Other specified congenital malformation syndromes affecting multiple systems). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.

Code	Description	Billable
Q87.0	Congenital malformation syndromes predominantly affecting facial appearance	✓
Q87.1	Congenital malformation syndromes predominantly associated with short stature	—
Q87.2	Congenital malformation syndromes predominantly involving limbs	✓
Q87.3	Congenital malformation syndromes involving early overgrowth	✓
Q87.4	Marfan syndrome	—
Q87.5	Other congenital malformation syndromes with other skeletal changes	✓
Q87.8	Other specified congenital malformation syndromes, not elsewhere classified	—
Q87.11	Prader-Willi syndrome	✓
Q87.19	Other congenital malformation syndromes predominantly associated with short stature	✓
Q87.40	Marfan syndrome, unspecified	✓
Q87.41	Marfan syndrome with cardiovascular manifestations	—
Q87.42	Marfan syndrome with ocular manifestations	✓
Q87.43	Marfan syndrome with skeletal manifestation	✓
Q87.81	Alport syndrome	✓
Q87.82	Arterial tortuosity syndrome	✓
Q87.83	Bardet-Biedl syndrome	✓
Q87.84	Laurence-Moon syndrome	✓
Q87.85	MED13L syndrome	✓
Q87.86	Kleefstra syndrome	✓
Q87.87	Hao-Fountain Syndrome	✓
Q87.88	CTNNB1 syndrome	✓
Q87.89	Other specified congenital malformation syndromes, not elsewhere classified	✓
Q87.410	Marfan syndrome with aortic dilation	✓
Q87.418	Marfan syndrome with other cardiovascular manifestations	✓

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