Q87: Other specified congenital malformation syndromes affecting multiple systems
Codes under Q87 (Other specified congenital malformation syndromes affecting multiple systems). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| Q87.0 | Congenital malformation syndromes predominantly affecting facial appearance | ✓ |
| Q87.0 | Congenital malformation syndromes predominantly affecting facial appearance | ✓ |
| Q87.1 | Congenital malformation syndromes predominantly associated with short stature | — |
| Q87.1 | Congenital malformation syndromes predominantly associated with short stature | — |
| Q87.2 | Congenital malformation syndromes predominantly involving limbs | ✓ |
| Q87.2 | Congenital malformation syndromes predominantly involving limbs | ✓ |
| Q87.3 | Congenital malformation syndromes involving early overgrowth | ✓ |
| Q87.3 | Congenital malformation syndromes involving early overgrowth | ✓ |
| Q87.4 | Marfan syndrome | — |
| Q87.4 | Marfan syndrome | — |
| Q87.5 | Other congenital malformation syndromes with other skeletal changes | ✓ |
| Q87.5 | Other congenital malformation syndromes with other skeletal changes | ✓ |
| Q87.8 | Other specified congenital malformation syndromes, not elsewhere classified | — |
| Q87.8 | Other specified congenital malformation syndromes, not elsewhere classified | — |
| Q87.11 | Prader-Willi syndrome | ✓ |
| Q87.11 | Prader-Willi syndrome | ✓ |
| Q87.19 | Other congenital malformation syndromes predominantly associated with short stature | ✓ |
| Q87.19 | Other congenital malformation syndromes predominantly associated with short stature | ✓ |
| Q87.40 | Marfan syndrome, unspecified | ✓ |
| Q87.40 | Marfan syndrome, unspecified | ✓ |
| Q87.41 | Marfan syndrome with cardiovascular manifestations | — |
| Q87.41 | Marfan syndrome with cardiovascular manifestations | — |
| Q87.42 | Marfan syndrome with ocular manifestations | ✓ |
| Q87.42 | Marfan syndrome with ocular manifestations | ✓ |
| Q87.43 | Marfan syndrome with skeletal manifestation | ✓ |
| Q87.43 | Marfan syndrome with skeletal manifestation | ✓ |
| Q87.81 | Alport syndrome | ✓ |
| Q87.81 | Alport syndrome | ✓ |
| Q87.82 | Arterial tortuosity syndrome | ✓ |
| Q87.82 | Arterial tortuosity syndrome | ✓ |
| Q87.83 | Bardet-Biedl syndrome | ✓ |
| Q87.83 | Bardet-Biedl syndrome | ✓ |
| Q87.84 | Laurence-Moon syndrome | ✓ |
| Q87.84 | Laurence-Moon syndrome | ✓ |
| Q87.85 | MED13L syndrome | ✓ |
| Q87.85 | MED13L syndrome | ✓ |
| Q87.86 | Kleefstra syndrome | ✓ |
| Q87.86 | Kleefstra syndrome | ✓ |
| Q87.87 | Hao-Fountain Syndrome | ✓ |
| Q87.87 | Hao-Fountain Syndrome | ✓ |
| Q87.88 | CTNNB1 syndrome | ✓ |
| Q87.88 | CTNNB1 syndrome | ✓ |
| Q87.89 | Other specified congenital malformation syndromes, not elsewhere classified | ✓ |
| Q87.89 | Other specified congenital malformation syndromes, not elsewhere classified | ✓ |
| Q87.410 | Marfan syndrome with aortic dilation | ✓ |
| Q87.410 | Marfan syndrome with aortic dilation | ✓ |
| Q87.418 | Marfan syndrome with other cardiovascular manifestations | ✓ |
| Q87.418 | Marfan syndrome with other cardiovascular manifestations | ✓ |
| Q87.A | Loeys-Dietz syndrome | ✓ |
Frequently asked questions
What is ICD-10-CM code Q87?
Q87 is an ICD-10-CM category covering Other specified congenital malformation syndromes affecting multiple systems. It contains 49 more specific diagnosis codes, 41 of which are billable.
Is Q87 a billable code?
No — Q87 is a category header and isn't billable on its own. Code to the highest level of specificity using one of its subcodes (for example Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance). 41 of the 49 codes under Q87 are billable.
What codes fall under Q87?
Q87 includes Q87.0, Q87.0, Q87.1, Q87.1, Q87.2, plus 44 more. See the full list with descriptions and billable status above.
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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