E78: Disorders of lipoprotein metabolism and other lipidemias
Codes under E78 (Disorders of lipoprotein metabolism and other lipidemias). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| E78.0 | Pure hypercholesterolemia | — |
| E78.0 | Pure hypercholesterolemia | — |
| E78.00 | Pure hypercholesterolemia, unspecified | ✓ |
| E78.00 | Pure hypercholesterolemia, unspecified | ✓ |
| E78.01 | Familial hypercholesterolemia | — |
| E78.01 | Familial hypercholesterolemia | — |
| E78.1 | Pure hyperglyceridemia | ✓ |
| E78.1 | Pure hyperglyceridemia | ✓ |
| E78.2 | Mixed hyperlipidemia | ✓ |
| E78.2 | Mixed hyperlipidemia | ✓ |
| E78.3 | Hyperchylomicronemia | ✓ |
| E78.3 | Hyperchylomicronemia | ✓ |
| E78.4 | Other hyperlipidemia | — |
| E78.4 | Other hyperlipidemia | — |
| E78.5 | Hyperlipidemia, unspecified | ✓ |
| E78.5 | Hyperlipidemia, unspecified | ✓ |
| E78.6 | Lipoprotein deficiency | ✓ |
| E78.6 | Lipoprotein deficiency | ✓ |
| E78.7 | Disorders of bile acid and cholesterol metabolism | — |
| E78.7 | Disorders of bile acid and cholesterol metabolism | — |
| E78.8 | Other disorders of lipoprotein metabolism | — |
| E78.8 | Other disorders of lipoprotein metabolism | — |
| E78.9 | Disorder of lipoprotein metabolism, unspecified | ✓ |
| E78.9 | Disorder of lipoprotein metabolism, unspecified | ✓ |
| E78.010 | Homozygous familial hypercholesterolemia [HoFH] | ✓ |
| E78.010 | Homozygous familial hypercholesterolemia [HoFH] | ✓ |
| E78.011 | Heterozygous familial hypercholesterolemia [HeFH] | ✓ |
| E78.011 | Heterozygous familial hypercholesterolemia [HeFH] | ✓ |
| E78.019 | Familial hypercholesterolemia, unspecified | ✓ |
| E78.019 | Familial hypercholesterolemia, unspecified | ✓ |
| E78.41 | Elevated Lipoprotein(a) | ✓ |
| E78.41 | Elevated Lipoprotein(a) | ✓ |
| E78.49 | Other hyperlipidemia | ✓ |
| E78.49 | Other hyperlipidemia | ✓ |
| E78.70 | Disorder of bile acid and cholesterol metabolism, unspecified | ✓ |
| E78.70 | Disorder of bile acid and cholesterol metabolism, unspecified | ✓ |
| E78.71 | Barth syndrome | ✓ |
| E78.71 | Barth syndrome | ✓ |
| E78.72 | Smith-Lemli-Opitz syndrome | ✓ |
| E78.72 | Smith-Lemli-Opitz syndrome | ✓ |
| E78.79 | Other disorders of bile acid and cholesterol metabolism | ✓ |
| E78.79 | Other disorders of bile acid and cholesterol metabolism | ✓ |
| E78.81 | Lipoid dermatoarthritis | ✓ |
| E78.81 | Lipoid dermatoarthritis | ✓ |
| E78.89 | Other lipoprotein metabolism disorders | ✓ |
| E78.89 | Other lipoprotein metabolism disorders | ✓ |
Frequently asked questions
What is ICD-10-CM code E78?
E78 is an ICD-10-CM category covering Disorders of lipoprotein metabolism and other lipidemias. It contains 46 more specific diagnosis codes, 36 of which are billable.
Is E78 a billable code?
No — E78 is a category header and isn't billable on its own. Code to the highest level of specificity using one of its subcodes (for example E78.0 — Pure hypercholesterolemia). 36 of the 46 codes under E78 are billable.
What codes fall under E78?
E78 includes E78.0, E78.0, E78.00, E78.00, E78.01, plus 41 more. See the full list with descriptions and billable status above.
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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