ICD-10-CM category
E76: Disorders of glycosaminoglycan metabolism
Codes under E76 (Disorders of glycosaminoglycan metabolism). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| E76.0 | Mucopolysaccharidosis, type I | — |
| E76.01 | Hurler's syndrome | ✓ |
| E76.1 | Mucopolysaccharidosis, type II | ✓ |
| E76.02 | Hurler-Scheie syndrome | ✓ |
| E76.2 | Other mucopolysaccharidoses | — |
| E76.03 | Scheie's syndrome | ✓ |
| E76.3 | Mucopolysaccharidosis, unspecified | ✓ |
| E76.8 | Other disorders of glucosaminoglycan metabolism | ✓ |
| E76.9 | Glucosaminoglycan metabolism disorder, unspecified | ✓ |
| E76.21 | Morquio mucopolysaccharidoses | — |
| E76.22 | Sanfilippo mucopolysaccharidoses | ✓ |
| E76.29 | Other mucopolysaccharidoses | ✓ |
| E76.210 | Morquio A mucopolysaccharidoses | ✓ |
| E76.211 | Morquio B mucopolysaccharidoses | ✓ |
| E76.219 | Morquio mucopolysaccharidoses, unspecified | ✓ |
More free billing tools: all ICD-10 categories · ICD-10 search · denial codes · Medicare fees
Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
Code the diagnosis right
Join providers across the country delivering modern virtual care with CareNiva. Free to start, ready in minutes.
100% Satisfaction Guaranteed — try it risk-free