E76: Disorders of glycosaminoglycan metabolism
Codes under E76 (Disorders of glycosaminoglycan metabolism). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| E76.0 | Mucopolysaccharidosis, type I | — |
| E76.0 | Mucopolysaccharidosis, type I | — |
| E76.01 | Hurler's syndrome | ✓ |
| E76.01 | Hurler's syndrome | ✓ |
| E76.1 | Mucopolysaccharidosis, type II | ✓ |
| E76.1 | Mucopolysaccharidosis, type II | ✓ |
| E76.02 | Hurler-Scheie syndrome | ✓ |
| E76.02 | Hurler-Scheie syndrome | ✓ |
| E76.2 | Other mucopolysaccharidoses | — |
| E76.2 | Other mucopolysaccharidoses | — |
| E76.03 | Scheie's syndrome | ✓ |
| E76.03 | Scheie's syndrome | ✓ |
| E76.3 | Mucopolysaccharidosis, unspecified | ✓ |
| E76.3 | Mucopolysaccharidosis, unspecified | ✓ |
| E76.8 | Other disorders of glucosaminoglycan metabolism | ✓ |
| E76.8 | Other disorders of glucosaminoglycan metabolism | ✓ |
| E76.9 | Glucosaminoglycan metabolism disorder, unspecified | ✓ |
| E76.9 | Glucosaminoglycan metabolism disorder, unspecified | ✓ |
| E76.21 | Morquio mucopolysaccharidoses | — |
| E76.21 | Morquio mucopolysaccharidoses | — |
| E76.22 | Sanfilippo mucopolysaccharidoses | ✓ |
| E76.22 | Sanfilippo mucopolysaccharidoses | ✓ |
| E76.29 | Other mucopolysaccharidoses | ✓ |
| E76.29 | Other mucopolysaccharidoses | ✓ |
| E76.210 | Morquio A mucopolysaccharidoses | ✓ |
| E76.210 | Morquio A mucopolysaccharidoses | ✓ |
| E76.211 | Morquio B mucopolysaccharidoses | ✓ |
| E76.211 | Morquio B mucopolysaccharidoses | ✓ |
| E76.219 | Morquio mucopolysaccharidoses, unspecified | ✓ |
| E76.219 | Morquio mucopolysaccharidoses, unspecified | ✓ |
Frequently asked questions
What is ICD-10-CM code E76?
E76 is an ICD-10-CM category covering Disorders of glycosaminoglycan metabolism. It contains 30 more specific diagnosis codes, 24 of which are billable.
Is E76 a billable code?
No — E76 is a category header and isn't billable on its own. Code to the highest level of specificity using one of its subcodes (for example E76.0 — Mucopolysaccharidosis, type I). 24 of the 30 codes under E76 are billable.
What codes fall under E76?
E76 includes E76.0, E76.0, E76.01, E76.01, E76.1, plus 25 more. See the full list with descriptions and billable status above.
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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