ICD-10-CM category
E72: Other disorders of amino-acid metabolism
Codes under E72 (Other disorders of amino-acid metabolism). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| E72.0 | Disorders of amino-acid transport | — |
| E72.00 | Disorders of amino-acid transport, unspecified | ✓ |
| E72.01 | Cystinuria | ✓ |
| E72.1 | Disorders of sulfur-bearing amino-acid metabolism | — |
| E72.02 | Hartnup's disease | ✓ |
| E72.2 | Disorders of urea cycle metabolism | — |
| E72.03 | Lowe's syndrome | ✓ |
| E72.3 | Disorders of lysine and hydroxylysine metabolism | ✓ |
| E72.04 | Cystinosis | ✓ |
| E72.4 | Disorders of ornithine metabolism | ✓ |
| E72.5 | Disorders of glycine metabolism | — |
| E72.8 | Other specified disorders of amino-acid metabolism | — |
| E72.09 | Other disorders of amino-acid transport | ✓ |
| E72.9 | Disorder of amino-acid metabolism, unspecified | ✓ |
| E72.10 | Disorders of sulfur-bearing amino-acid metabolism, unspecified | ✓ |
| E72.11 | Homocystinuria | ✓ |
| E72.12 | Methylenetetrahydrofolate reductase deficiency | ✓ |
| E72.19 | Other disorders of sulfur-bearing amino-acid metabolism | ✓ |
| E72.20 | Disorder of urea cycle metabolism, unspecified | ✓ |
| E72.21 | Argininemia | ✓ |
| E72.22 | Arginosuccinic aciduria | ✓ |
| E72.23 | Citrullinemia | ✓ |
| E72.29 | Other disorders of urea cycle metabolism | ✓ |
| E72.50 | Disorder of glycine metabolism, unspecified | ✓ |
| E72.51 | Non-ketotic hyperglycinemia | ✓ |
| E72.52 | Trimethylaminuria | ✓ |
| E72.53 | Primary hyperoxaluria | — |
| E72.54 | Secondary hyperoxaluria | — |
| E72.59 | Other disorders of glycine metabolism | ✓ |
| E72.81 | Disorders of gamma aminobutyric acid metabolism | ✓ |
| E72.89 | Other specified disorders of amino-acid metabolism | ✓ |
| E72.530 | Primary hyperoxaluria, type 1 | ✓ |
| E72.538 | Other specified primary hyperoxaluria | ✓ |
| E72.539 | Primary hyperoxaluria, unspecified | ✓ |
| E72.540 | Dietary hyperoxaluria | ✓ |
| E72.541 | Enteric hyperoxaluria | ✓ |
| E72.548 | Other secondary hyperoxaluria | ✓ |
| E72.549 | Secondary hyperoxaluria, unspecified | ✓ |
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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