ICD-10-CM category
E70: Disorders of aromatic amino-acid metabolism
Codes under E70 (Disorders of aromatic amino-acid metabolism). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| E70.0 | Classical phenylketonuria | ✓ |
| E70.1 | Other hyperphenylalaninemias | ✓ |
| E70.2 | Disorders of tyrosine metabolism | — |
| E70.3 | Albinism | — |
| E70.4 | Disorders of histidine metabolism | — |
| E70.5 | Disorders of tryptophan metabolism | ✓ |
| E70.8 | Other disorders of aromatic amino-acid metabolism | — |
| E70.9 | Disorder of aromatic amino-acid metabolism, unspecified | ✓ |
| E70.20 | Disorder of tyrosine metabolism, unspecified | ✓ |
| E70.21 | Tyrosinemia | ✓ |
| E70.29 | Other disorders of tyrosine metabolism | ✓ |
| E70.30 | Albinism, unspecified | ✓ |
| E70.31 | Ocular albinism | — |
| E70.32 | Oculocutaneous albinism | — |
| E70.33 | Albinism with hematologic abnormality | — |
| E70.39 | Other specified albinism | ✓ |
| E70.40 | Disorders of histidine metabolism, unspecified | ✓ |
| E70.41 | Histidinemia | ✓ |
| E70.49 | Other disorders of histidine metabolism | ✓ |
| E70.81 | Aromatic L-amino acid decarboxylase deficiency | ✓ |
| E70.89 | Other disorders of aromatic amino-acid metabolism | ✓ |
| E70.310 | X-linked ocular albinism | ✓ |
| E70.311 | Autosomal recessive ocular albinism | ✓ |
| E70.318 | Other ocular albinism | ✓ |
| E70.319 | Ocular albinism, unspecified | ✓ |
| E70.320 | Tyrosinase negative oculocutaneous albinism | ✓ |
| E70.321 | Tyrosinase positive oculocutaneous albinism | ✓ |
| E70.328 | Other oculocutaneous albinism | ✓ |
| E70.329 | Oculocutaneous albinism, unspecified | ✓ |
| E70.330 | Chediak-Higashi syndrome | ✓ |
| E70.331 | Hermansky-Pudlak syndrome | ✓ |
| E70.338 | Other albinism with hematologic abnormality | ✓ |
| E70.339 | Albinism with hematologic abnormality, unspecified | ✓ |
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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