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ICD-10-CM category

E70: Disorders of aromatic amino-acid metabolism

33 subcodes · 26 billable · Look up any code with the ICD-10 search

Codes under E70 (Disorders of aromatic amino-acid metabolism). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.

CodeDescriptionBillable
E70.0Classical phenylketonuria
E70.1Other hyperphenylalaninemias
E70.2Disorders of tyrosine metabolism
E70.3Albinism
E70.4Disorders of histidine metabolism
E70.5Disorders of tryptophan metabolism
E70.8Other disorders of aromatic amino-acid metabolism
E70.9Disorder of aromatic amino-acid metabolism, unspecified
E70.20Disorder of tyrosine metabolism, unspecified
E70.21Tyrosinemia
E70.29Other disorders of tyrosine metabolism
E70.30Albinism, unspecified
E70.31Ocular albinism
E70.32Oculocutaneous albinism
E70.33Albinism with hematologic abnormality
E70.39Other specified albinism
E70.40Disorders of histidine metabolism, unspecified
E70.41Histidinemia
E70.49Other disorders of histidine metabolism
E70.81Aromatic L-amino acid decarboxylase deficiency
E70.89Other disorders of aromatic amino-acid metabolism
E70.310X-linked ocular albinism
E70.311Autosomal recessive ocular albinism
E70.318Other ocular albinism
E70.319Ocular albinism, unspecified
E70.320Tyrosinase negative oculocutaneous albinism
E70.321Tyrosinase positive oculocutaneous albinism
E70.328Other oculocutaneous albinism
E70.329Oculocutaneous albinism, unspecified
E70.330Chediak-Higashi syndrome
E70.331Hermansky-Pudlak syndrome
E70.338Other albinism with hematologic abnormality
E70.339Albinism with hematologic abnormality, unspecified

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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.

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