Q00: Anencephaly and similar malformations
Codes under Q00 (Anencephaly and similar malformations). A ✓ marks a billable (fully specified) code; category codes without a ✓ are not billable on their own.
| Code | Description | Billable |
|---|---|---|
| Q00.0 | Anencephaly | ✓ |
| Q00.0 | Anencephaly | ✓ |
| Q00.1 | Craniorachischisis | ✓ |
| Q00.1 | Craniorachischisis | ✓ |
| Q00.2 | Iniencephaly | ✓ |
| Q00.2 | Iniencephaly | ✓ |
Frequently asked questions
What is ICD-10-CM code Q00?
Q00 is an ICD-10-CM category covering Anencephaly and similar malformations. It contains 6 more specific diagnosis codes, 6 of which are billable.
Is Q00 a billable code?
No — Q00 is a category header and isn't billable on its own. Code to the highest level of specificity using one of its subcodes (for example Q00.0 — Anencephaly). 6 of the 6 codes under Q00 are billable.
What codes fall under Q00?
Q00 includes Q00.0, Q00.0, Q00.1, Q00.1, Q00.2, plus 1 more. See the full list with descriptions and billable status above.
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Informational only, not coding or medical advice. Verify against the official ICD-10-CM (FY2026) and your payer's guidelines.
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